Antibody data
- Antibody Data
- Antigen structure
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- Product number
- BS8946 - Provider product page
- Provider
- Bioworld Technology, Inc
- Product name
- GNS polyclonal antibody
- Antibody type
- Polyclonal
- Antigen
- N-acetylglucosamine-6-sulfatase; Glucosamine-6-sulfatase; G6S; GNS
- Description
- The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
- Reactivity
- Human, Mouse, Rat
- Host
- Rabbit
- Isotype
- IgG
- Vial size
- 100ul
- Concentration
- 1 mg/ml
- Storage
- Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.
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