BS8946

antibody from Bioworld Technology, Inc
Targeting: GNS
Provider product page for BS8946
Western blot
Immunohistochemistry

Antibody data

Product number
BS8946 - Provider product page
Provider
Bioworld Technology, Inc
Product name
GNS polyclonal antibody
Antibody type
Polyclonal
Antigen
N-acetylglucosamine-6-sulfatase; Glucosamine-6-sulfatase; G6S; GNS
Description
The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
Reactivity
Human, Mouse, Rat
Host
Rabbit
Isotype
IgG
Vial size
100ul
Concentration
1 mg/ml
Storage
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.
GNS protein structure - BS8946 shown in red.