Antibody data
- Antibody Data
- Antigen structure
- References [1]
- Comments [0]
- Validations
- Western blot [1]
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Validation data
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- Product number
- H00002132-B01 - Provider product page
- Provider
- Abnova Corporation
- Proper citation
- Abnova Corporation Cat#H00002132-B01, RRID:AB_1113655
- Product name
- EXT2 MaxPab mouse polyclonal antibody (B01)
- Antibody type
- Polyclonal
- Description
- Mouse polyclonal antibody raised against a full-length human EXT2 protein.
- Antigen sequence
MCASVKYNIRGPALIPRMKTKHRIYYITLFSIVLL
GLIATGMFQFWPHSIESSNDWNVEKRSIRDVPVVR
LPADSPIPERGDLSCRMHTCFDVYRCGFNPKNKIK
VYIYALKKYVDDFGVSVSNTISREYNELLMAISDS
DYYTDDINRACLFVPSIDVLNQNTLRIKETAQAMA
QLSRWDRGTNHLLFNMLPGGPPDYNTALDVPRDRA
LLAGGGFSTWTYRQGYDVSIPVYSPLSAEVDLPEK
GPGPRQYFLLSSQVGLHPEYREDLEALQVKHGESV
LVLDKCTNLSEGVLSVRKRCHKHQVFDYPQVLQEA
TFCVVLRGARLGQAVLSDVLQAGCVPVVIADSYIL
PFSEVLDWKRASVVVPEEKMSDVYSILQSIPQRQI
EEMQRQARWFWEAYFQSIKAIALATLQIINDRIYP
YAAISYEEWNDPPAVKWGSVSNPLFLPLIPPQSQG
FTAIVLTYDRVESLFRVITEVSKVPSLSKLLVVWN
NQNKNPPEDSLWPKIRVPLKVVRTAENKLSNRFFP
YDEIETEAVLAIDDDIIMLTSDELQFGYEVWREFP
DRLVGYPGRLHLWDHEMNKWKYESEWTNEVSMVLT
GAAFYHKYFNYLYTYKMPGDIKNWVDAHMNCEDIA
MNFLVANVTGKAVIKVTPRKKFKCPECTAIDGLSL
DQTHMVERSECINKFASVFGTMPLKVVEHRADPVL
YKDDFPEKLKSFPNIGSL- Storage
- Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
Submitted references Old gene, new phenotype: mutations in heparan sulfate synthesis enzyme, EXT2 leads to seizure and developmental disorder, no exostoses.
Farhan SM, Wang J, Robinson JF, Prasad AN, Rupar CA, Siu VM, FORGE Canada Consortium, Hegele RA
Journal of medical genetics 2015 Oct;52(10):666-75
Journal of medical genetics 2015 Oct;52(10):666-75
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Supportive validation
- Submitted by
- Abnova Corporation (provider)
- Main image
- Experimental details
- Western Blot analysis of EXT2 expression in transfected 293T cell line (H00002132-T01) by EXT2 MaxPab polyclonal antibody.Lane 1: EXT2 transfected lysate(78.98 KDa).Lane 2: Non-transfected lysate.