BS8208

antibody from Bioworld Technology, Inc
Targeting: AAAS
Provider product page for BS8208
Western blot
Immunohistochemistry

Antibody data

Product number
BS8208 - Provider product page
Provider
Bioworld Technology, Inc
Product name
AAAS polyclonal antibody
Antibody type
Polyclonal
Antigen
Recombinant full length Human AAAS.
Description
Aladin (Adracalin) belongs to a family of WD repeat-containing proteins. These proteins have a wide variety of functions, including signal transduction regulation, RNA processing and transcription. Aladin plays a role in peripheral and central nervous system development. It is widely expressed, with the highest expression seen in pituitary gland, corpus callosum, cerebellum, adrenal gland and gastrointestinal structures. Defects in Aladin cause the autosomal recessive disorder achalasia-addisonianism-alacrima (triple A) syndrome. Triple A syndrome is characterized by achalasia, alacrima and adrenocortico-tropin-resistant adrenal insufficiency. Robust expression in neural systems associated with cognitive, motor and sensory functions is consistent with the myriad of symptoms experienced by patients with triple A syndrome.
Reactivity
Human
Host
Rabbit
Isotype
IgG
Vial size
100ul
Concentration
1 mg/ml
Storage
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.
AAAS protein structure - BS8208 shown in red.