FNab03748

antibody from FineTest Biotech

Targeting: HADHA GBP, LCEH, LCHAD, MTPA

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Validation data

Product number: FNab03748 - Provider product page
Provider: FineTest Biotech
Product name: HADHA antibody
Antibody type: Polyclonal
Antigen: Recombinant protein fragment
Description: This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.
Reactivity: Human, Mouse, Rat
Host: Rabbit
Conjugate: Unconjugated
Antigen sequence: hydroxyacyl-Coenzyme A dehydrogenas e/3-ketoacyl-Coenzyme A thiolase/en oyl-Coenzyme A hydratase (trifuncti onal protein), alpha subunit
Epitope: IgG
Isotype: IgG
Vial size: 100¦Ìg
Concentration: Immunogen affinity purified
Storage: PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20¡æ for 12 months (Avoid repeated freeze / thaw cycles.)
Handling: PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20¡æ for 12 months (Avoid repeated freeze / thaw cycles.)

HADHA protein structure - FNab03748 shown in red.