ABIN2845755

antibody from antibodies-online

Targeting: GAA

Western blot (Supportive data in Antibodypedia)

Immunohistochemistry (Supportive data in Antibodypedia)

Antibody Data

Product number

ABIN2845755

Provider

antibodies-online

Product name

anti-Glucosidase, Alpha, Acid (GAA) (AA 174-203), (N-Term) antibody

Antibody type

Polyclonal

Description

This antibody is purified through a protein A column, followed by peptide affinity purification.

Reactivity

Human

Host

Rabbit

Epitope

AA 174-203, N-Term

Antibody clone number

RB18979

Vial size

80 μL

Storage

GAA Antibody (N-term) can be refrigerated at 2-8°C for up to 6 months. For long term storage, place the at -20°C.

References

Submitted references

Molecular features of 23 patients with glycogen storage disease type III in Turkey: a novel mutation p.R1147G associated with isolated glucosidase deficiency, along with 9 AGL mutations.

Aoyama Y, Ozer I, Demirkol M, Ebara T, Murase T, Podskarbi T, Shin YS, Gokcay G, Okubo M
Journal of human genetics 2009 Nov;54(11):681-6

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Silent exonic mutation in the acid-alpha-glycosidase gene that causes glycogen storage disease type II by affecting mRNA splicing.

Maimaiti M, Takahashi S, Okajima K, Suzuki N, Ohinata J, Araki A, Tanaka H, Mukai T, Fujieda K
Journal of human genetics 2009 Aug;54(8):493-6

Western blot

Supportive validation

Submitted by

antibodies-online (provider)

Main image

Experimental details

WB

Supportive validation

Submitted by

antibodies-online (provider)

Main image

Experimental details

WB

Immunohistochemistry

Supportive validation

Submitted by

antibodies-online (provider)

Main image

Experimental details

IHC

Supportive validation

Submitted by

antibodies-online (provider)

Main image

Experimental details

IHC