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- Antigen structure
- References [9]
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- Product number
- ABIN2839247 - Provider product page
- Provider
- antibodies-online
- Product name
- anti-Amylo-alpha-1, 6-Glucosidase, 4-alpha-Glucanotransferase (AGL) (AA 1479-1510), (C-Term) antibody
- Antibody type
- Polyclonal
- Description
- This antibody is prepared by Saturated Ammonium Sulfate (SAS) precipitation followed by dialysis against PBS.
- Reactivity
- Human
- Host
- Rabbit
- Epitope
- AA 1479-1510, C-Term
- Antibody clone number
- RB4978
- Vial size
- 80 μL
- Storage
- Maintain refrigerated at 2-8°C for up to 6 months. For long term storage store at -20°C in small aliquots to prevent freeze-thaw cycles.
Submitted references Laforin-malin complex degrades polyglucosan bodies in concert with glycogen debranching enzyme and brain isoform glycogen phosphorylase.
Anti-retinal antibodies in patients with macular telangiectasia type 2.
Genetic depletion of the malin E3 ubiquitin ligase in mice leads to lafora bodies and the accumulation of insoluble laforin.
Fast-twitch sarcomeric and glycolytic enzyme protein loss in inclusion body myositis.
A role for AGL ubiquitination in the glycogen storage disorders of Lafora and Cori's disease.
Mutational and haplotype analysis of AGL in patients with glycogen storage disease type III.
Human glycogen debranching enzyme gene (AGL): complete structural organization and characterization of the 5' flanking region.
Molecular cloning and nucleotide sequence of cDNA encoding human muscle glycogen debranching enzyme.
Assignment of the human glycogen debrancher gene to chromosome 1p21.
Liu Y, Zeng L, Ma K, Baba O, Zheng P, Liu Y, Wang Y
Molecular neurobiology 2014 Apr;49(2):645-57
Molecular neurobiology 2014 Apr;49(2):645-57
Anti-retinal antibodies in patients with macular telangiectasia type 2.
Zhu L, Shen W, Zhu M, Coorey NJ, Nguyen AP, Barthelmes D, Gillies MC
Investigative ophthalmology & visual science 2013 Aug 21;54(8):5675-83
Investigative ophthalmology & visual science 2013 Aug 21;54(8):5675-83
Genetic depletion of the malin E3 ubiquitin ligase in mice leads to lafora bodies and the accumulation of insoluble laforin.
DePaoli-Roach AA, Tagliabracci VS, Segvich DM, Meyer CM, Irimia JM, Roach PJ
The Journal of biological chemistry 2010 Aug 13;285(33):25372-81
The Journal of biological chemistry 2010 Aug 13;285(33):25372-81
Fast-twitch sarcomeric and glycolytic enzyme protein loss in inclusion body myositis.
Parker KC, Kong SW, Walsh RJ, Bch., Salajegheh M, Moghadaszadeh B, Amato AA, Nazareno R, Lin YY, Krastins B, Sarracino DA, Beggs AH, Pinkus JL, Greenberg SA
Muscle & nerve 2009 Jun;39(6):739-53
Muscle & nerve 2009 Jun;39(6):739-53
A role for AGL ubiquitination in the glycogen storage disorders of Lafora and Cori's disease.
Cheng A, Zhang M, Gentry MS, Worby CA, Dixon JE, Saltiel AR
Genes & development 2007 Oct 1;21(19):2399-409
Genes & development 2007 Oct 1;21(19):2399-409
Mutational and haplotype analysis of AGL in patients with glycogen storage disease type III.
Horinishi A, Okubo M, Tang NL, Hui J, To KF, Mabuchi T, Okada T, Mabuchi H, Murase T
Journal of human genetics 2002;47(2):55-9
Journal of human genetics 2002;47(2):55-9
Human glycogen debranching enzyme gene (AGL): complete structural organization and characterization of the 5' flanking region.
Bao Y, Dawson TL Jr, Chen YT
Genomics 1996 Dec 1;38(2):155-65
Genomics 1996 Dec 1;38(2):155-65
Molecular cloning and nucleotide sequence of cDNA encoding human muscle glycogen debranching enzyme.
Yang BZ, Ding JH, Enghild JJ, Bao Y, Chen YT
The Journal of biological chemistry 1992 May 5;267(13):9294-9
The Journal of biological chemistry 1992 May 5;267(13):9294-9
Assignment of the human glycogen debrancher gene to chromosome 1p21.
Yang-Feng TL, Zheng K, Yu J, Yang BZ, Chen YT, Kao FT
Genomics 1992 Aug;13(4):931-4
Genomics 1992 Aug;13(4):931-4
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Supportive validation
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