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- Antigen structure
- References [7]
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- Validations
- Western blot [1]
- Immunohistochemistry [1]
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- Product number
- 10175-2-AP - Provider product page
- Provider
- Proteintech Group
- Proper citation
- Proteintech Cat#10175-2-AP, RRID:AB_2259019
- Product name
- BCS1L antibody
- Antibody type
- Polyclonal
- Description
- BCS1L antibody (Cat. #10175-2-AP) is a rabbit polyclonal antibody that shows reactivity with human, mouse, rat and has been validated for the following applications: IF, IHC, WB,ELISA.
- Reactivity
- Human, Mouse, Rat
- Host
- Rabbit
- Conjugate
- Unconjugated
- Isotype
- IgG
- Vial size
- 20ul, 150ul
Submitted references Distinct Roles of Mitochondrial HIGD1A and HIGD2A in Respiratory Complex and Supercomplex Biogenesis.
LYRM7/MZM1L is a UQCRFS1 chaperone involved in the last steps of mitochondrial Complex III assembly in human cells.
Molecular diagnosis of infantile mitochondrial disease with targeted next-generation sequencing.
Cellular pathophysiological consequences of BCS1L mutations in mitochondrial complex III enzyme deficiency.
How do human cells react to the absence of mitochondrial DNA?
Assembly of the oxidative phosphorylation system in humans: what we have learned by studying its defects.
Impaired complex III assembly associated with BCS1L gene mutations in isolated mitochondrial encephalopathy.
Timón-Gómez A, Garlich J, Stuart RA, Ugalde C, Barrientos A
Cell reports 2020 May 5;31(5):107607
Cell reports 2020 May 5;31(5):107607
LYRM7/MZM1L is a UQCRFS1 chaperone involved in the last steps of mitochondrial Complex III assembly in human cells.
Sánchez E, Lobo T, Fox JL, Zeviani M, Winge DR, Fernández-Vizarra E
Biochimica et biophysica acta 2013 Mar;1827(3):285-93
Biochimica et biophysica acta 2013 Mar;1827(3):285-93
Molecular diagnosis of infantile mitochondrial disease with targeted next-generation sequencing.
Calvo SE, Compton AG, Hershman SG, Lim SC, Lieber DS, Tucker EJ, Laskowski A, Garone C, Liu S, Jaffe DB, Christodoulou J, Fletcher JM, Bruno DL, Goldblatt J, Dimauro S, Thorburn DR, Mootha VK
Science translational medicine 2012 Jan 25;4(118):118ra10
Science translational medicine 2012 Jan 25;4(118):118ra10
Cellular pathophysiological consequences of BCS1L mutations in mitochondrial complex III enzyme deficiency.
Morán M, Marín-Buera L, Gil-Borlado MC, Rivera H, Blázquez A, Seneca S, Vázquez-López M, Arenas J, Martín MA, Ugalde C
Human mutation 2010 Aug;31(8):930-41
Human mutation 2010 Aug;31(8):930-41
How do human cells react to the absence of mitochondrial DNA?
Mineri R, Pavelka N, Fernandez-Vizarra E, Ricciardi-Castagnoli P, Zeviani M, Tiranti V
PloS one 2009 May 28;4(5):e5713
PloS one 2009 May 28;4(5):e5713
Assembly of the oxidative phosphorylation system in humans: what we have learned by studying its defects.
Fernández-Vizarra E, Tiranti V, Zeviani M
Biochimica et biophysica acta 2009 Jan;1793(1):200-11
Biochimica et biophysica acta 2009 Jan;1793(1):200-11
Impaired complex III assembly associated with BCS1L gene mutations in isolated mitochondrial encephalopathy.
Fernandez-Vizarra E, Bugiani M, Goffrini P, Carrara F, Farina L, Procopio E, Donati A, Uziel G, Ferrero I, Zeviani M
Human molecular genetics 2007 May 15;16(10):1241-52
Human molecular genetics 2007 May 15;16(10):1241-52
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Supportive validation
- Submitted by
- Proteintech Group (provider)
- Main image
- Experimental details
- A549 cells were subjected to SDS PAGE followed by western blot with 10175-2-AP(BCS1L antibody) at dilution of 1:1000
- Sample type
- cell line
Supportive validation
- Submitted by
- Proteintech Group (provider)
- Main image
- Experimental details
- The BCS1L antibody from Proteintech is a rabbit polyclonal antibody to a recombinant protein of human BCS1L. This antibody recognizes human, mouse, rat antigen. The BCS1L antibody has been validated for the following applications: ELISA, WB, IHC analysis.
