Tissue expression
Cell line expression
Protein structure

LRPPRC

Leucine rich pentatricopeptide repeat containing
GP130, LRP130, LSFC 
This gene encodes a leucine-rich protein that has multiple pentatricopeptide repeats (PPR). The precise role of this protein is unknown but studies suggest it may play a role in cytoskeletal organization, vesicular transport, or in transcriptional regulation of both nuclear and mitochondrial genes. The protein localizes primarily to mitochondria and is predicted to have an N-terminal mitochondrial targeting sequence. Mutations in this gene are associated with the French-Canadian type of Leigh syndrome. [provided by RefSeq, Mar 2012]
More gene data

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163 antibodies from 28 providers.

Antibody properties

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AntibodyRefsTypeWBELICCIPIHCFC
Proteintech Group
4 antibodies
Atlas Antibodies
2 antibodies
Invitrogen Antibodies
16 antibodies
NSJ Bioreagents
1 antibody
GeneTex
3 antibodies
Boster Biological Technology
2 antibodies
antibodies-online
58 antibodies
Cusabio Biotech Co., Ltd
6 antibodies
Novus Biologicals
4 antibodies
NovoPro Bioscience Inc.
3 antibodies
OriGene
2 antibodies
Aviva Systems Biology
2 antibodies
Abnova Corporation
1 antibody
Signalway Antibody LLC
1 antibody
St John's Laboratory
2 antibodies
Affinity Biosciences
1 antibody
Bethyl Laboratories
1 antibody
Wuhan Fine Biotech Co., Ltd.
1 antibody
RabMAbs
1 antibody
MyBioSource
5 antibodies
Creative Diagnostics
5 antibodies
Abbexa
8 antibodies
MilliporeSigma / Merck KGaA
2 antibodies
United States Biological
12 antibodies
Leading Biology
2 antibodies
ProSci
1 antibody
Creative Biolabs
3 antibodies